50-198-2900

Glucosamine 6 sulfatase Rabbit anti-Human, Polyclonal, Bioss

Manufacturer: Bioss

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Pack Size SKU Availability Price
Each of 1 50-198-2900-Each-of-1 In Stock ₹ 38,381.25

50-198-2900 - Each of 1

₹ 38,381.25

In Stock

Quantity

1

Base Price: ₹ 38,381.25

GST (18%): ₹ 6,908.625

Total Price: ₹ 45,289.875

Antigen

Glucosamine 6 sulfatase

Classification

Polyclonal

Conjugate

Unconjugated

Gene

GNS

Gene Alias

2610016K11Rik; AU042285; BOS_5599; C87209; G6S; glucosamine (N-acetyl)-6-sulfatase; glucosamine (N-acetyl)-6-sulfatase (Sanfilippo disease IIID); glucosamine -6-sulfatase; Glucosamine-6-sulfatase; Gns; N28088; N-acetylglucosamine 6-sulfatase precursor; N-acetylglucosamine-6-sulfatase

Host Species

Rabbit

Purification Method

Protein A

Regulatory Status

RUO

Gene ID (Entrez)

2799

Content And Storage

-20°C

Form

Liquid

Applications

Immunofluorescence, Immunohistochemistry (Paraffin), Western Blot

Concentration

1 μg/mL

Formulation

PBS with 1% BSA, 50% glycerol and 0.09% sodium azide; pH

Gene Accession No.

P15586

Gene Symbols

GNS

Immunogen

KLH conjugated synthetic peptide derived from human GNS/Glucosamine 6 sulfatase.

Quantity

100 μL

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Isotype

IgG

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Description

  • GNS is a lysosomal enzyme found in all cells
  • It is involved in the catabolism of heparin, heparan sulphate, and keratan sulphate
  • Deficiency of this enzyme results in the accumulation of undegraded substrate and the lysosomal storage disorder mucopolysaccharidosis type IIID (Sanfilippo D syndrome)
  • Mucopolysaccharidosis type IIID is the least common of the four subtypes of Sanfilippo syndrome.