89-014-140

lipase A, lysosomal acid, cholesterol esterase, Mouse, Clone: 1F9, Abnova™

Manufacturer: Abnova Corporation

Select a Size

Pack Size SKU Availability Price
Each of 1 89-014-140-Each-of-1 In Stock ₹ 42,898.00

89-014-140 - Each of 1

₹ 42,898.00

In Stock

Quantity

1

Base Price: ₹ 42,898.00

GST (18%): ₹ 7,721.64

Total Price: ₹ 50,619.64

Antigen

lipase A, lysosomal acid, cholesterol esterase

Classification

Monoclonal

Conjugate

Unconjugated

Formulation

PBS with no preservative; pH 7.4

Gene Accession No.

BC012287

Gene Symbols

LIPA

Immunogen

LIPA (AAH12287, 1 a.a. ∼ 399 a.a) full-length recombinant protein with GST tag. MW of the GST tag alone is 26 KDa.

Quantity

100 μg

Primary or Secondary

Primary

Target Species

Human

Product Type

Antibody

Applications

ELISA, Immunoprecipitation, Western Blot

Clone

1F9

Description

Mouse monoclonal antibody raised against a full length recombinant LIPA.

Gene

LIPA

Gene Alias

CESD/LAL

Host Species

Mouse

Purification Method

Affinity Purified

Regulatory Status

RUO

Gene ID (Entrez)

3988

Content And Storage

Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.

Isotype

IgG2b κ

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Description

  • This gene encodes lipase A, the lysosomal acid lipase (also known as cholesterol ester hydrolase)
  • This enzyme functions in the lysosome to catalyze the hydrolysis of cholesteryl esters and triglycerides
  • Mutations in this gene can result in Wolman disease and cholesteryl ester storage disease
  • Alternatively spliced transcript variants encoding the same protein have been found for this gene
  • [provided by RefSeq Sequence: MKMRFLGLVVCLVLWPLHSEGSGGKLTALDPETNMNVSEIISYWGFPSEEYLVETEDGYILCLNRIPHGRKNHSDKGPKPVVFLQHGLLADSSNWVTNLANSSLGFILADAGFDVWMGNSRGNTWSRKHKTLSVSQDEFWAFSYDEMAKYDLPASINFILNKTGQEQVYYVGHSQGTTIGFIAFSQIPELAKRIKMFFALGPVASVAFCTSPMAKLGRLPDHLIKDLFGDKEFLPQSAFLKWLGTHVCTHVILKELCGNLCFLLCGFNERNLNMSRVDVYTTHSPAGTSVQNMLHWSQAVKFQKFQAFDWGSSAKNYFHYNQSYPPTYNVKDMLVPTAVWSGGHDWLADVYDVNILLTQITNLVFHESIPEWEHLDFIWGLDAPWRLYNKIINLMRKYQ