89-022-248
GAA, Mouse, Clone: 3C6, Abnova™
Manufacturer: Abnova Corporation
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | 89-022-248-Each-of-1 | In Stock | ₹ 44,411.00 |
89-022-248 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 44,411.00
GST (18%): ₹ 7,993.98
Total Price: ₹ 52,404.98
Antigen
GAA
Classification
Monoclonal
Conjugate
Unconjugated
Formulation
PBS with no preservative; pH 7.4
Gene Accession No.
BC040431
Gene Symbols
GAA
Immunogen
GAA (AAH40431, 851 a.a. ∼ 952 a.a) partial recombinant protein with GST tag. MW of the GST tag alone is 26 KDa.
Quantity
100 μg
Primary or Secondary
Primary
Target Species
Human
Product Type
Antibody
Isotype
IgG1 κ
Applications
ELISA, Western Blot
Clone
3C6
Description
Mouse monoclonal antibody raised against a partial recombinant GAA.
Gene
GAA
Gene Alias
LYAG
Host Species
Mouse
Purification Method
Affinity chromatography
Regulatory Status
RUO
Gene ID (Entrez)
2548
Content And Storage
Store at -20°C or lower. Aliquot to avoid repeated freezing and thawing.
Form
Liquid
Related Products
Description
- This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes
- Different forms of acid alpha-glucosidase are obtained by proteolytic processing
- Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum
- Three transcript variants encoding the same protein have been found for this gene
- [provided by RefSeq] Sequence: GEARGELFWDDGESLEVLERGAYTQVIFLARNNTIVNELVRVTSEGAGLQLQKVTVLGVATAPQQVLSNGVPVSNFTYSPDTKVLDICVSLLMGEQFLVSWC