PIMA541589
alpha Galactosidase Monoclonal Antibody (C8), Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PIMA541589-Each-of-1 | In Stock | ₹ 44,989.50 |
PIMA541589 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 44,989.50
GST (18%): ₹ 8,098.11
Total Price: ₹ 53,087.61
Antigen
alpha Galactosidase
Classification
Monoclonal
Concentration
1 mg/mL
Formulation
PBS with 50% glycerol and 0.05% ProClin 300
Gene Accession No.
P06280
Gene Symbols
GLA
Immunogen
Recombinant protein Galactosidase Alpha. The antigen corresponds to amino acid range 81-429 of the target protein.
Quantity
200 μL
Primary or Secondary
Primary
Target Species
Human
Product Type
Antibody
Isotype
IgG2b κ
Applications
Immunohistochemistry (Paraffin), Western Blot
Clone
C8
Conjugate
Unconjugated
Gene
GLA
Gene Alias
Agalsidase; agalsidase alfa; Ags; Alpha-D-galactosidase A; alpha-D-galactoside galactohydrolase; alpha-D-galactoside galactohydrolase 1; alpha-gal A; alpha-galactosidase A; GALA; galactosidase alpha; galactosidase, alpha; GLA; Melibiase
Host Species
Mouse
Purification Method
Protein A/G
Regulatory Status
RUO
Gene ID (Entrez)
2717
Content And Storage
-20°C
Form
Liquid
Related Products
Description
- This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins
- This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose
- A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.