GAA Polyclonal Antibody, Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PIPA5117464-Each-of-1 | In Stock | ₹ 46,502.50 |
PIPA5117464 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 46,502.50
GST (18%): ₹ 8,370.45
Total Price: ₹ 54,872.95
Antigen
GAA
Classification
Polyclonal
Conjugate
Unconjugated
Gene
Gaa
Gene Alias
70 kDa lysosomal alpha-glucosidase; 76 kDa lysosomal alpha-glucosidase; acid (Pompe disease, glycogen storage disease type II); acid alpha-glucosidase; acid maltase; Aglucosidase alfa; E430018M07Rik; Gaa; glucosidase alpha, acid; glucosidase, alpha, acid; glucosidase, alpha; acid (Pompe disease, glycogen storage disease type II); LYAG; Lysosomal alpha-glucosidase
Host Species
Rabbit
Purification Method
Protein G
Regulatory Status
RUO
Gene ID (Entrez)
14387, 2548
Content And Storage
-20°C or -80°C if preferred
Form
Liquid
Applications
Immunocytochemistry, Immunohistochemistry (Paraffin), Western Blot
Concentration
2.595 mg/mL
Formulation
10mM PBS with 50% glycerol and 0.03% ProClin 300; pH 7.4
Gene Accession No.
P10253, P70699
Gene Symbols
Gaa
Immunogen
Recombinant Human Lysosomal alpha-glucosidase protein (601-952aa)
Quantity
100 μg
Primary or Secondary
Primary
Target Species
Human, Mouse
Product Type
Antibody
Isotype
IgG
Related Products
Description
- This antibody has been tested in direct-ELISA This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes
- Different forms of acid alpha-glucosidase are obtained by proteolytic processing
- Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum
- Three transcript variants encoding the same protein have been found for this gene.