GAA Recombinant Rabbit Monoclonal Antibody (5E5), Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | FEMA550114-Each-of-1 | In Stock | ₹ 37,202.00 |
FEMA550114 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 37,202.00
GST (18%): ₹ 6,696.36
Total Price: ₹ 43,898.36
Antigen
GAA
Classification
Recombinant Monoclonal
Concentration
0.8 mg/mL
Formulation
PBS with 50% glycerol and 0.02% sodium azide, pH 7.4
Gene Accession No.
P10253
Gene Symbols
Gaa
Immunogen
A synthesized peptide derived from Human GAA
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human
Form
Liquid
Applications
ELISA, Immunohistochemistry (Paraffin)
Clone
5E5
Conjugate
Unconjugated
Gene
Gaa
Gene Alias
70 kDa lysosomal alpha-glucosidase, 76 kDa lysosomal alpha-glucosidase, acid (Pompe disease, glycogen storage disease type II), acid alpha-glucosidase, acid maltase, Aglucosidase alfa, E430018M07Rik, Gaa, glucosidase alpha, acid, glucosidase, alpha, acid, glucosidase, alpha, acid (Pompe disease, glycogen storage disease type II), LYAG, Lysosomal alpha-glucosidase
Host Species
Rabbit
Purification Method
Affinity chromatography
Regulatory Status
RUO
Gene ID (Entrez)
2548
Content And Storage
-20°C or -80°C if preferred
Isotype
IgG
Related Products
Description
- This gene encodes acid alpha-glucosidase, which is essential for the degradation of glycogen to glucose in lysosomes
- Different forms of acid alpha-glucosidase are obtained by proteolytic processing
- Defects in this gene are the cause of glycogen storage disease II, also known as Pompe's disease, which is an autosomal recessive disorder with a broad clinical spectrum
- Three transcript variants encoding the same protein have been found for this gene.