TRPML1 Polyclonal Antibody, Invitrogen™
Manufacturer: Thermo Scientific
Select a Size
| Pack Size | SKU | Availability | Price |
|---|---|---|---|
| Each of 1 | PA146474-Each-of-1 | In Stock | ₹ 46,947.50 |
PA146474 - Each of 1
In Stock
Quantity
1
Base Price: ₹ 46,947.50
GST (18%): ₹ 8,450.55
Total Price: ₹ 55,398.05
Antigen
TRPML1
Classification
Polyclonal
Conjugate
Unconjugated
Gene
MCOLN1
Gene Alias
2210015I05Rik; MCLN1; Mcoln1; MCOLN1 mucolipin 1; MG-2; MGC7172; ML1; ML4; MLIV; MST080; MSTP080; Mucolipidin; mucolipidosis type IV protein; mucolipin 1; mucolipin-1; Transient receptor potential channel mucolipin 1; Transient receptor potential-mucolipin 1; TRPML1; TRP-ML1; TRPM-L1
Host Species
Rabbit
Purification Method
Antigen affinity chromatography
Regulatory Status
RUO
Gene ID (Entrez)
288371, 57192, 94178
Content And Storage
Store at 4°C short term. For long term storage, store at -20°C, avoiding freeze/thaw cycles.
Form
Liquid
Applications
Western Blot
Concentration
1.0 mg/mL
Formulation
PBS with 0.02% sodium azide
Gene Accession No.
Q99J21, Q9GZU1
Gene Symbols
MCOLN1
Immunogen
Synthetic peptide corresponding to residues 500-580 of a C-terminal portion of mouse Mucolipin-1. [Swiss-Prot# Q99J21]
Quantity
100 μL
Primary or Secondary
Primary
Target Species
Human, Mouse, Rat
Product Type
Antibody
Isotype
IgG
Related Products
Description
- The target sequence has 85% sequence homology with monkey and 78% sequence homology with bovine
- Suggested positive control: mouse brain protein
- Defects in Mucolipin-1 are the cause of mucolipidosis type IV (MLIV), also known as sialolipidosis
- MLIV is an autosomal recessive lysosomal storage disorder characterized by severe psychomotor retardation and ophthalmologic abnormalities, including corneal opacity, retinal degeneration and strabismus
- Storage bodies of lipids and water-soluble substances are seen by electron microscopy in almost every cell type of the patients
- Most patients are unable to speak or walk independently and reach a maximal developmental level of 1-2 years
- All patients have constitutive achlorhydia associated with a secondary elevation of serum gastrin levels.